• Users Online: 397
  • Print this page
  • Email this page
CASE REPORT
Year : 2021  |  Volume : 4  |  Issue : 2  |  Page : 121-124

Role of preoperative multidetector computed tomography airway reconstruction in anaesthetic management of mucopolysaccharidosis type IV


1 Department of Anaesthesiology and Critical Care, Seven Hills Hospital, Mumbai, Maharashtra, India
2 Department of Anaesthesiology, Seth GS Medical College and KEM Hospital, Mumbai, Maharashtra, India

Correspondence Address:
Dr. Pradeep Tiwari
Department of Anaesthesiology and Critical Care, Seven Hills Hospital, Marol, Andheri East, Mumbai - 400 059, Maharashtra
India
Login to access the Email id

Source of Support: None, Conflict of Interest: None


DOI: 10.4103/arwy.arwy_33_21

Rights and Permissions

Mucopolysaccharidoses (MPS) are a group of lysosomal storage disorders that often present with a difficult airway. The trachea is usually narrowed and flattened, making the choice of correct technique and endotracheal tube (ETT) size crucial. Multidetector computed tomography (MDCT) images have been used to assess the airway of children who are considered at risk for difficult intubation. However, it has not been standardised in preoperative assessment of MPS. We report a case in whom after failed fibreoptic intubation, titrated doses of injection propofol were given and direct laryngoscopy was performed. A 6.0 mm internal diameter (ID) and later a 5.0 mm ID ETT were tried but could not be negotiated. Subsequently, the airway was secured with a 4.5 mm ID ETT. Postoperatively, MDCT airway reconstruction demonstrated that the narrowest part of airway measured 4.3 mm. Anaesthesiologists often face a multitude of challenges in these patients. Our experience gained in retrospect suggests that a detailed preoperative evaluation including MDCT airway reconstruction, followed by meticulous planning, is essential for a safe outcome.


[FULL TEXT] [PDF]*
Print this article     Email this article
 Next article
 Previous article
 Table of Contents

 Similar in PUBMED
   Search Pubmed for
   Search in Google Scholar for
 Related articles
 Citation Manager
 Access Statistics
 Reader Comments
 Email Alert *
 Add to My List *
 * Requires registration (Free)
 

 Article Access Statistics
    Viewed280    
    Printed12    
    Emailed0    
    PDF Downloaded18    
    Comments [Add]    

Recommend this journal